Atresia pulmonar con septum integro pdf

Pulmonary atresia with intact ventricular septum paivs is a rare congenital malformation. Pulmonary atresia with intact ventricular septum paivs is a relatively uncommon form of congenital heart disease and is remarkable in its morphologic diversity, characterized by varying degrees of right ventricle rv hypoplasia and associated with tricuspid valve dysplasia and sinusoidal right ventriculocoronary connections. This blockage prevents the flow of blood to the lungs. Atresia pulmonar con septum interventricular intacto. Caracteristicas morfologicas angiograficas na atresia. Atresia pulmonar con comun icacion interventricular gustavo a. Atresia pulmonar con tabique interventricular integro. Pulmonary atresia with intact interventricular septum. Atresia pulmonar con septo integro connecting repositories. In this form of pulmonary atresia, the wall, or septum, between the ventricles remains complete and intact. Jun 02, 2011 pulmonary atresia and ventricular septal defect and truncus arteriosus lan nguyen, md duration. Atresia pulmonar con septum interventricular intacto scielo cuba. Atresia pulmonar con tabique interventricular integro en una cardiopata congnita ciantica con flujo pulmonar disminuido y cardiomegalia.

Atresia pulmonar con septo integro bive ntricular uno y medio glenn univentricular fontan figura 3. Atresia pulmonar con septo integro asociada a estenosis aortica. The valve is completely closed thereby obstructing the outflow of blood from the heart to the lungs. Pulmonary atresia and ventricular septal defect and truncus arteriosus lan nguyen, md duration. A single uniform approach in the management of this disease is. Gabriel cassalet bustillo, md atresia pulmonar con septo interventricular integro manuel r. Pdf atresia pulmonar con septo integro researchgate. Paivs involves complete blockage of the pulmonary valve located on the right side of the heart. Houston methodist debakey cv education 2,7 views 12. Pulmonary atresia with intact interventricular septum paivs is a subtype of pulmonary atresia that presents as cyanotic congenital heart disease.

Atresia pulmonar con septo interventricular intacto y. Atresia pulmonar con septo integro article pdf available in cirugia cardiovascular 212 april 2014 with 43 reads how we measure reads. Pathology paivs is the combination of obstruction of the pulmonary outflow tract from pulmona. The pulmonary valve is located on the right side of the heart between the right ventricle and pulmonary artery. Perforacion y valvuloplastia pulmonar mediante tecnica mecanica modificada. Pulmonary atresia with intact ventricular septum paivs and critical pulmonary stenosis cps are rare forms of cyanotic congenital heart disease 1,2 where pulmonary blood flow depends on the ductus arteriosus. Pulmonary atresia with intact ventricular septum and critical pulmonary stenosis in newborns encompasses a wide spectrum of disease, including cases with significant right ventricular hypoplasia and coronary artery to right ventricle fistulae, which may be considered a contraindication for decompression of the right ventricle. Percutaneous management of pulmonary atresia with intact. Pulmonary atresia with an intact ventricular septum. Atresia pulmonar com septo integroatresia pulmonar com septo integro definicao. Atresia pulmonar com comunicacao interventricular cardio. There is significant morphologic heterogeneity among patients with paivs, 3 and the selection criteria for univentricular or biventricular repair are under debate.

In patients with pulmonary atresia with intact ventricular septum paivs, radiofrequencyassisted perforation of the valve is the most widely used initial therapy. Atresia pulmonar con comunicacion interventricular. Atresia pulmonar con septo integro biventricular 60% fontan 24% uno y medio 12% paliacion 3% trasplante 1% figura 4. Atresia pulmonar con septum interventricular integro. Congenital heart defects facts about pulmonary atresia cdc. Atresia pulmonar con comunicacion interventricular cirugia. Atresia pulmonar con septo integro cirugia cardiovascular. Pulmonary atresia with intact ventricular septum percutaneous. The influence of ventricular morphology and coronary artery dominance and morphology on early mortality in patients with pulmonary atresia and intact ventricular septum. Gonzalez morejon1 ansia serrano sanchez2 giselle serrano ricardo1. Pdf pulmonary atresia with intact ventricular septum is an apparently simple cyanotic congenital heart disease. Pulmonary atresia with intact ventricular septum is an. During pregnancy when the heart is developing, very little blood flows into or out of the right ventricle rv, and therefore the rv doesnt fully develop and remains very small.